Abstract for presentation at 13th International Congress on Oral Pathology and Medicine

Osteoglophonic dysplasia – oral and dental implication

  • Tina Roberts, University of the Western Cape, South Africa
  • P Beighton, University of Cape Town, South Africa
  • Lawrence Stephen, University of the Western Cape, South Africa

    • Aims and Objectives: Documentation of oral and dental implications of osteoglophonic dysplasia.
    Settings and Participants: We had recently reviewed the oral and dental manifestations of a female with Osteoglophonic Dysplasia, aged 39 years who was first documented three decades ago.
    Results: This rare genetic disorder showed gross stunting of stature and was associated with severe craniofacial malformation and multiple unerupted teeth. Radiographically, multiple lucent lesions were present in the tubular bones and mandible and several impacted teeth were inverted.
    Conclusion: We concluded that prosthetic dental replacement in our patient would be difficult because of the distorted bony relationships and large alveolar ridges. Equally, craniofacial reconstruction might be compromised by obstruction of the nasal airways, difficulty in intubation and post-operative respiratory problems.

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